Takayasu arteritis: presenting as hypertensive encephalopathy at 9 year of age

Abstract

Abstract: Takayasu Arthritis (TA) is a rare chronic granulomatous large vessel vaculitis, rarely diagnosed in first decade of life. A 9 year old female child presented to us with multiple episode of generalized convulsions and encephalopathy. B/L upper limb low volume pulse and low BP, B/L lower limb good volume pulse and high blood pressure, papilledema of both eye on examination, early diastolic murmur in mitral area and Doppler study showed sluggish flow in both upper limb vesssels, MRA showed stenosis of both subclavian, vertebral(cervical part) and CCA. Case diagnosed as Takayasu Arteritis, mild AR and hypertensive encephalopathy. Patient was put on steroids, on follow up blood pressure was not under control and referred for angioplasty. Here we report case TA at 9 year of age presenting hypertensive encephalopathy.